Spontaneous haemothorax: a cause of sudden death in von Recklinghausen's disease.

Griffiths, A P; White, J; Dawson, A · Postgrad Med J · 1998

case_report · Level V

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Abstract

Vasculopathy is a relatively frequent but poorly recognised manifestation of von Recklinghausen's neurofibromatosis. One of its more dramatic presentations is as spontaneous haemothorax. Clinicians and pathologists should be aware of this syndrome as a cause of sudden death in patients with neurofibromatosis.

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