Unusual fan shaped ossification in a female fetus with radiological features of boomerang dysplasia.

Odent, S; Loget, P; Le Marec, B; Delezoïde, A L; Maroteaux, P · J Med Genet · 1999

case_report · Level V

Where this comes from

Abstract

We report on a female fetus of 24 weeks whose clinical and radiological findings were compatible with boomerang dysplasia (BD). However, histopathology was unusual with a lateral fan shaped diaphyseal ossification. This has never been described either in typical atelosteogenesis I (AT-I) or in BD. The purpose of this report is to find out if this condition is a separate lethal bone dysplasia or another histological feature of the nosological group of AT-I and BD.

Medical subject headings