Anaesthetic management of patients with mucopolysaccharidosis IV presenting for major orthopaedic surgery.
case_report · Level V
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- Record sourced from PubMed, PMID 10408824.
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Abstract
Mucopolysaccharidosis IV, also known as Morquio-Brailsford syndrome, is an inherited autosomal recessive disorder of mucopolysaccharide metabolism leading to accumulation of keratan sulphate in the connective tissue of multiple organ systems. Based on a case report, the anaesthetic implications for the treatment of patients with MPS IV presenting for major orthopaedic surgery are discussed.
Medical subject headings
- Anesthesia
- Mucopolysaccharidosis IV
- Orthopedics