Adult-onset angiofibroma and multiple endocrine neoplasia type I.
case_report · Level V
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- Record sourced from PubMed, PMID 10534680.
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Abstract
Multiple endocrine neoplasia type 1 (MEN 1) predisposes affected persons to neoplasms of the parathyroid glands, the endocrine pancreas, the anterior pituitary, and the duodenum. We report the first case of adult-onset multiple angiofibromas of the central face associated with MEN 1. Seven siblings also developed adult-onset angiofibromas, none with evidence of tuberous sclerosis. Basic fibroblast growth factor (BFGF) is elevated in many patients with MEN 1 and may play a pathogenetic role.
Medical subject headings
- Angiofibroma
- Multiple Endocrine Neoplasia Type 1
- Skin Neoplasms