A novel X-linked dominant condition: X-linked congenital isolated ptosis.

McMullan, T F; Collins, A R; Tyers, A G; Robinson, D O · Am J Hum Genet · 2000

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Abstract

We present a large family with a previously undescribed condition: X-linked dominant congenital bilateral isolated ptosis. Linkage analysis defined a critical region between Xq24 and Xq27.1, with a maximum single-point LOD score of 2.88 at DXS1047 and DXS984. Male and female family members are equally affected, providing an example of an X-linked, truly dominant condition.

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