Congenital dyserythropoietic anemia type I presenting as persistent pulmonary hypertension of the newborn.

Shalev, H; Moser, A; Kapelushnik, J; Karplus, M; Zucker, N; Yaniv, I; Tamary, H · J Pediatr · 2000

case_report · Level V

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Abstract

Congenital dyserythropoietic anemia (CDA) is a rare group of inherited bone marrow disorders characterized by anemia with ineffective erythropoiesis. We report 3 siblings from a family known to have CDA type I who presented with persistent pulmonary hypertension of the newborn (PPHN). We suggest that the diagnosis of CDA type I should be considered in any neonate with PPHN and anemia.

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