Fechtner's syndrome: considerations of anesthetic management.

Mertzlufft, F; Koster, A; Steinhart, H; Schenk, J F; Crystal, G J · Anesth Analg · 2000

case_report · Level V

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Abstract

Fechtner's syndrome is a rare form of macrothrombocytopenia (potentially associated with other hemostatic deficiencies, e.g., von Willebrand's disease and protein Z deficiency), which can exacerbate the risk of uncontrollable bleeding during surgery. We describe the management of a patient with Fechtner's syndrome involving desmopressin, prednisone, and platelets, which produced safe and effective results during cochlear implant surgery.

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