Natural history of cardiac involvement in myotonic dystrophy: correlation with CTG repeats.

Antonini, G; Giubilei, F; Mammarella, A; Amicucci, P; Fiorelli, M; Gragnani, F; Morino, S; Ceschin, P V et al. · Neurology · 2000

prospective_cohort · Level II

Where this comes from

Abstract

The authors prospectively studied the natural course of cardiac involvement and its relationship to cytosine-thymine-guanine (CTG) expansion in 50 patients with myotonic dystrophy who were submitted to periodic cardiovascular EKG and EKG-Holter monitoring during a median follow-up of 56 months. Nineteen patients (38%) developed major EKG changes. CTG length was not correlated with the frequency of EKG abnormalities, but was inversely correlated with the age at onset of EKG abnormalities (p < 0.0001). CTG length influences the timing of cardiac complications in myotonic dystrophy.

Medical subject headings