B-cell lymphoma in a patient with WHIM syndrome.

Chae, K M; Ertle, J O; Tharp, M D · J Am Acad Dermatol · 2001

case_report · Level V

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Abstract

WHIM syndrome is a rare congenital familial syndrome consisting of warts, hypogammaglobulinemia, infections, and myelokathexis. We describe a 30-year-old man with WHIM syndrome, in whom red dermal facial nodules developed. The diagnosis of B-cell lymphoma was established with biopsy and immunohistochemical studies. To our knowledge, this is the first reported case of WHIM syndrome complicated by a B-cell lymphoma.

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