Isolated diffuse mesangial sclerosis and Wilms tumor suppressor gene.

Ito, S; Takata, A; Hataya, H; Ikeda, M; Kikuchi, H; Hata, J; Honda, M · J Pediatr · 2001

case_series · Level IV

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Abstract

Diffuse mesangial sclerosis is a rare renal disease, occurring either in isolation or as part of Denys-Drash syndrome. Denys-Drash syndrome originates from mutations of the Wilms tumor suppressor gene (WT1 ). We describe the presence of WT1 mutations in 7 Japanese children with isolated diffuse mesangial sclerosis.

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