Acute fatty liver of pregnancy associated with short-chain acyl-coenzyme A dehydrogenase deficiency.

Matern, D; Hart, P; Murtha, A P; Vockley, J; Gregersen, N; Millington, D S; Treem, W R · J Pediatr · 2001

case_report · Level V

Where this comes from

Abstract

There is a correlation between pregnancy complications such as acute fatty liver of pregnancy and long-chain 3-hydroxyacyl-coenzyme A dehydrogenase (LCHAD) deficiency. We diagnosed another fatty acid beta-oxidation defect, short-chain acyl-coenzyme A dehydrogenase deficiency, in an infant when evaluating him because his mother had acute fatty liver of pregnancy. Other beta-oxidation defects, in addition to LCHAD deficiency, should be considered in children born after pregnancies complicated by liver disease.

Medical subject headings