Hirschsprung disease associated with severe cartilage-hair hypoplasia.

Mäkitie, O; Kaitila, I; Rintala, R · J Pediatr · 2001

case_control · Level III

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Abstract

Cartilage-hair hypoplasia is a chondrodysplasia with a high incidence of Hirschsprung disease. This study suggests that Hirschsprung disease is associated especially with severe cartilage-hair hypoplasia: the patients with Hirschsprung disease had severe growth failure and a higher incidence of alopecia, infections, malignancies, and childhood anemia than the patients with cartilage-hair hypoplasia who did not have Hirschsprung disease.

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