Malignant eccrine poroma with spinal and cerebrospinal fluid metastases: case report.

Abstract

A rare case of metastasizing malignant eccrine poroma (porocarcinoma) is described. This case is unique because metastasis resulted in hydrocephalus in the cerebrospinal fluid and spinal cord compression in the lumbar spine. A 57-year-old man presented with acute confusion, lower limb weakness, and urinary concerns. Investigation revealed acute hydrocephalus and extradural cord compression of the lumbar spine. The acute hydrocephalous was treated with a ventriculoperitoneal shunt. The spinal cord and conus were decompressed by laminectomy and supplemented with pedicular screw fixation. The case reported here is the first with metastases from a malignant eccrine poroma causing spinal cord compression and acute hydrocephalus. Our observation is compared with a review of the literature.