Chylothorax complicating Gorham's disease.

Chavanis, N; Chaffanjon, P; Frey, G; Vottero, G; Brichon, P Y · Ann Thorac Surg · 2001

case_report · Level V

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Abstract

Gorham's disease is a rare disorder characterized by a proliferation of thin-walled lymphatic vessels (lymphangiectasia) resulting in an osteolysis. A chylothorax is present in about one-fifth of the patients and carries a poor prognosis. In this circumstance, surgery including thoracic duct ligation, pleurodesis, and excision of involved tissue is probably the treatment of choice. It is facilitated by a precise radiological assessment using a computed tomographic scanning coupled with a lymphography. We report such a case.

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