Hereditary benign intraepithelial dyskeratosis: Report of two cases with prominent oral lesions.
case_report · Level V
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Abstract
Hereditary benign intraepithelial dyskeratosis is a rare autosomal dominant disorder of the oral and ocular mucosa initially described in the Haliwa-Saponi Native American tribe of North Carolina. We describe 2 sisters with the characteristic oral and ocular findings. This entity should be distinguished from several other diseases that cause white lesions in the mouth including white sponge nevus.
Medical subject headings
- Conjunctiva
- Dyskeratosis Congenita
- Mouth Mucosa