Thyroid dysgenesis caused by PAX8 mutation: the hypermutability with CpG dinucleotides at codon 31.

Komatsu, M; Takahashi, T; Takahashi, I; Nakamura, M; Takahashi, I; Takada, G · J Pediatr · 2001

case_report · Level V

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Abstract

We identified a novel mutation (CGC to T GC) at codon 31 of the Paired box 8 gene, an important transcription factor in the development of the thyroid gland. Mutations at this codon have been independently reported in 2 cases (CGC to CA C). These transitions are considered typical CpG-consequence mutations and account for hypermutability at this position.

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