Interferon-gamma receptor deficiency mimicking Langerhans' cell histiocytosis.

Edgar, J D; Smyth, A E; Pritchard, J; Lammas, D; Jouanguy, E; Hague, R; Novelli, V; Dempsey, S et al. · J Pediatr · 2001

case_report · Level V

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Abstract

Two patients who were initially given a diagnosis of Langerhans' cell histiocytosis on the basis of the clinical, radiologic, and biopsy findings had mycobacterial infection subsequently identified. The correct diagnosis of dominant partial interferon-gamma receptor deficiency was established.

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