Leber's hereditary optic neuropathy (LHON/11778) with myoclonus: report of two cases.

Carelli, V; Valentino, M L; Liguori, R; Meletti, S; Vetrugno, R; Provini, F; Mancardi, G L; Bandini, F et al. · J Neurol Neurosurg Psychiatry · 2001

case_report · Level V

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Abstract

The previously unrecognised association of myoclonus in two patients with LHON with the 11778/ND4 pathogenic mutation is described. EEG failed to disclose epileptic figures, and a back averaging study suggested that myoclonus was cortical in origin in both patients.

Medical subject headings