MR cholangiography in the diagnosis of sclerosing cholangitis in Langerhans' cell histiocytosis.

König, C W; Pfannenberg, C; Trübenbach, J; Remy, C; Böhmer, G M; Ruck, P; Claussen, C D · Eur Radiol · 2001

case_report · Level V

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Abstract

Langerhans' cell histiocytosis (LCH) is a disorder of histiocytic proliferation that primarily affects infants. Imaging findings of a rare case of lung and liver involvement in an adult are presented. High-resolution computed tomography (HRCT) of the lungs showed confluent thin-walled cystic air spaces compatible with advanced LCH. Liver CT and MRI revealed unspecific signs of fatty infiltration. Irregular widening of peripheral bile ducts was displayed in breath-hold MR cholangiography. This pattern is considered characteristic for sclerosing cholangitis and should support the diagnosis of LCH in case of concomitant cystic pulmonary disease, even in adult patients.

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