Hyperzincemia with systemic inflammation: a heritable disorder of calprotectin metabolism with rheumatic manifestations?

Saito, Yoshiaki; Saito, Kayoko; Hirano, Yukiko; Ikeya, Kiyoko; Suzuki, Haruko; Shishikura, Keiko; Manno, Sumie; Takakuwa, Yuichi et al. · J Pediatr · 2002

case_report · Level V

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Abstract

A boy had infantile-onset systemic inflammation, growth failure, hepatosplenomegaly, anemia, leukocytopenia, progressive muscular dystrophy, and hypercalprotectinemia, resulting in marked hyperzincemia. His mother had a history of chronic arthritis since childhood and also showed hypercalprotectinemia/hyperzincemia. We postulate an inherent defect in calprotectin metabolism.

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