Meningioma presenting with Cushing's syndrome: an unusual clinical presentation.

Pecori Giraldi, Francesca; Terreni, Maria Rosa; Andreotti, Claudia; Losa, Marco; Lanzi, Roberto; Pontiroli, Antonio E; Cavagnini, Francesco · Ann Neurol · 2003

case_report · Level V

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Abstract

We report a patient with a meningioma presenting with Cushing's syndrome, an unprecedented paraneoplastic presentation. Molecular studies, bioassay, and high-performance liquid chromatography of tumor specimens demonstrated the synthesis and secretion of bioactive corticotropin-releasing hormone. To our knowledge, this appears to be the first report of a hormone-secreting meningioma and, further, the first clearly proven case of Cushing's syndrome due to ectopic corticotropin-releasing hormone secretion without concomitant corticotropin production.

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