IgA pemphigus occurring in a 1-month-old infant.

Suzuki, Masayuki; Karube, Sachiko; Kobori, Youichi; Usui, Keitaro; Murata, Satoru; Kato, Hideyuki; Nakagawa, Hidemi · J Am Acad Dermatol · 2003

case_report · Level V

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Abstract

An 11-month-old girl had recurrent pruritic vesiculopustular lesions involving the trunk, extremities, and scalp since the age of 1-month. Histopathologic examination revealed an intraepidermal bulla produced by acantholysis and neutrophilic spongiosis. Direct immunofluorescence showed IgA deposits in the intercellular space throughout the epidermis. Circulating anti-intercellular IgA autoantibodies were absent. Dapsone therapy was effective.

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