Hemopneumothorax associated with Marfan syndrome and congenital afibrinogenemia.
case_report · Level V
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- Record sourced from PubMed, PMID 12683581.
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Abstract
In patients with afibrinogenemia who require operation, prophylaxis against bleeding is important. We report the case of a 14-year-old boy with Marfan syndrome and congenital afibrinogenemia in whom hemopneumothorax developed. Video-assisted thoracoscopic surgery was performed successfully under intravenous administration of fibrinogen and with careful monitoring of plasma fibrinogen level.
Medical subject headings
- Afibrinogenemia
- Hemopneumothorax
- Marfan Syndrome