Chylotamponade: an unusual presentation of Gorham's syndrome.

Swelstad, Matthew Reed; Frumiento, Carmine; Garry-McCoy, Alice; Agni, Rashmi; Weigel, Tracey L · Ann Thorac Surg · 2003

case_report · Level V

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Abstract

Gorham's Syndrome, also known as massive osteolysis or "vanishing bone disease" results from lymphangiomatosis with adjacent bone resorption. Chylothorax is a common complication in cases of mediastinal involvement. We report a case of Gorham's Syndrome presenting as chylotamponade successfully treated with pericardial drainage, early parenteral nutritional support, bilateral pleurodesis for chylous effusions, and adjuvant external beam radiation.

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