Fatal interstitial pulmonary fibrosis in anti-Jo-1-negative amyopathic dermatomyositis.

High, Whitney A; Cohen, Jack B; Murphy, Bettina A; Costner, Melissa I · J Am Acad Dermatol · 2003

case_report · Level V

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Abstract

Amyopathic dermatomyositis (DM) describes a subpopulation with the cutaneous eruption of DM, but without muscle involvement. Interstitial pulmonary fibrosis is a recognized complication of DM, often correlated with antisynthetase enzymes, such as anti-Jo-1. We describe a case of fatal IPF in a patient with anti-Jo-1 antibody-negative amyopathic DM.

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