De novo t(X;21)(q28;q11) in a girl with phenotypic features of Williams-Beuren syndrome.

Telvi, L; Pinard, J M; Ion, R; Sinet, P M; Nicole, A; Feingold, J; Dulac, O; Pompidou, A et al. · J Med Genet · 1992

case_report · Level V

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Abstract

We describe a female infant with mental retardation and some of the phenotypic features of Williams-Beuren syndrome. Chromosome analysis showed t(X;21)(q28;q11). Diagnosis, inactivation of the X chromosome, and possible involvement of the translocation breakpoints in the pathogenesis of this syndrome are discussed.

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