Inflammatory pseudotumor of the heart with vasculitis and venous thrombosis.

Stark, P; Sandbank, J C; Rudnicki, C; Zahavi, I · Chest · 1992

case_report · Level V

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Abstract

Inflammatory pseudotumor (IPT) is a tumor-like reactive lesion of unknown etiology. An unusual case of intracardiac IPT with multisystemic involvement, including leukocytoclastic vasculitis, polyarthritis, and inferior vena cava thrombosis in a 17-year-old boy is reported. This unique combination may suggest that immune/autoimmune factors are important in the pathogenesis of IPT.

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