Bilateral sensorineural deafness in adenosine deaminase-deficient severe combined immunodeficiency.

Albuquerque, Wendy; Gaspar, Hubert B · J Pediatr · 2004

case_report · Level V

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Abstract

Adenosine deaminase deficiency presents with severe combined immunodeficiency and is treatable by bone marrow transplantation. With improved survival, the nonimmunologic manifestations of this condition are becoming apparent. We report a high incidence of bilateral sensorineural deafness in transplanted patients, which highlights the systemic nature of the disease.

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