Interleukin receptor-associated kinase (IRAK-4) deficiency associated with bacterial infections and failure to sustain antibody responses.

Day, Noorbibi; Tangsinmankong, Nutthapong; Ochs, Hans; Rucker, Rajivi; Picard, Capucine; Casanova, Jean-Laurent; Haraguchi, Soichi; Good, Robert · J Pediatr · 2004

case_report · Level V

Where this comes from

Abstract

We previously described a girl with recurrent episodes of pneumococcal pneumonia with septicemia and other infections,(1) found to have interleukin-1 receptor-associated kinase 4 deficiency (IRAK-4) deficiency.(2) In this report, we show that our patient is unable to sustain antibody responses either to polysaccharide or protein antigens or to a neoantigen-bacteriophage.

Medical subject headings