Destructive arthritis in a patient with Haim-munk syndrome.

Lidar, Merav; Zlotogorski, Abraham; Langevitz, Pnina; Tweezer-Zaks, Nurit; Zandman-Goddard, Gisele · J Rheumatol · 2004

case_report · Level V

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Abstract

Haim-Munk and Papillon-Lefèvre are 2 closely related syndromes, inherited in an autosomal recessive pattern, manifested by palmoplantar keratoderma and early, destructive periodontitis. Recently, mutations in the cathepsin C gene have been recognized in both syndromes. We describe a patient with Haim-Munk syndrome (palmar plantar keratosis and periodontitis) and destructive arthritis of the wrists and shoulder joints, an association that has not been previously described.

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