Paraneoplastic "stiff person syndrome" with metastatic adenocarcinoma and anti-Ri antibodies.

McCabe, D J H; Turner, N C; Chao, D; Leff, A; Gregson, N A; Womersley, H J; Mak, I; Perkin, G D et al. · Neurology · 2004

case_report · Level V

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Abstract

A 43-year-old woman presented with clinical and electrophysiologic features of stiff person syndrome (SPS), without abdominal or lumbar paraspinal muscle involvement. Investigations revealed metastatic adenocarcinoma of the lung with positive anti-Ri antibodies. Her clinical condition improved with diazepam, baclofen, tizanidine, and palliative chemotherapy. Screening for an underlying malignancy and anti-Ri antibodies should be considered in patients with SPS when clinical presentation is atypical.

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