Fatal pulmonary arterial hypertension complicating noncirrhotic portal fibrosis.

Goenka, M K; Mehta, S K; Malik, A K; Kumar, Y R; Kochhar, R · Am J Gastroenterol · 1992

case_report · Level V

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Abstract

A 25-yr-old female with noncirrhotic portal fibrosis underwent a lienorenal shunt for variceal bleed. Ten years after shunt surgery, she presented with progressive breathlessness, and severe pulmonary arterial hypertension was detected, to which she subsequently succumbed. Autopsy revealed classical plexogenic pulmonary arteriopathy.

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