Neuro-Behcet disease with predominant involvement of the brainstem.

Mirsattari, Seyed M; McGinn, Gregory J; Halliday, William C · Neurology · 2004

case_report · Level V

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Abstract

We report a patient with relapsing-remitting meningoencephalitis secondary to neuro-Behcet disease which resulted in recurrent brainstem encephalitis. MRI revealed increased signal intensity on the proton density and T2-weighted images and gadolinium enhancement during relapses. Autopsy revealed acute on chronic meningoencephalomyelitis involving the entire CNS, which was most marked in the brainstem.

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