Early occurrence of end-stage renal disease in a patient with infantile nephropathic cystinosis.

Schnaper, H W; Cottel, J; Merrill, S; Marcusson, E; Kissane, J M; Shackelford, G D; So, S K; Nelson, R D et al. · J Pediatr · 1992

case_report · Level V

Where this comes from

Abstract

We report the case of a patient with infantile nephropathic cystinosis who required renal transplantation at age 30 months. Exhaustive evaluation did not identify a cause of progressive renal failure other than cystinosis. The patient's genetic lesion was allelic with those of other patients with cystinosis; fusion of this patient's fibroblasts with fibroblasts from another patient with infantile nephropathic cystinosis did not demonstrate complementation of the biochemical defect.

Medical subject headings