Long-term survival in severe combined immune deficiency: the role of persistent maternal engraftment.

Tezcan, Ilhan; Ersoy, Fugen; Sanal, Ozden; Turul, Tuba; Uckan, Duygu; Balci, Sevim; Hicsonmez, Gonul; Prieur, M et al. · J Pediatr · 2005

case_report · Level V

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Abstract

Two siblings with severe combined immune deficiency, one with maternal engraftment and detectable immunologic functions who was alive at the age of 8 years are presented. Both patients had the same JAK3 gene mutation, suggesting that maternal engraftment may result in immune competence leading to long-term survival in patients with severe combined immune deficiency.

Medical subject headings