Spanish family with myalgia and cramps syndrome.

Sánchez-Arjona, M B; Rodríguez-Uranga, J J; Giles-Lima, M; Fernández-García, R; Chinchón-Lara, I; Antiñolo, G; Bautista-Lorite, J · J Neurol Neurosurg Psychiatry · 2005

case_report · Level V

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Abstract

A Spanish family is reported with dystrophinopathy of myalgia and cramps syndrome type. There were five affected males and three females, and also six asymptomatic carriers. Muscle biopsy showed a dystrophic pattern, but immunohistochemistry carried out with three anti-dystrophin antibodies was normal. Dystrophin analysis by western blot revealed a dystrophin of reduced quantity and molecular weight. DNA analysis showed a deletion of the dystrophin gene involving exons 45-52. The natural history of this disorder and the large intrafamilial clinical variability are discussed.

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