FcgammaRIIIb and complement component C7 codeficiency in a patient with recurrence of fulminant meningococcal septic shock.

Debard, Anne-Lise; Lamy, Brigitte; Monneret, Guillaume; Mira, Jean-Paul; Pachot, Alexandre; Kleijer, Marion; Aillaud, Marie-Françoise; Boibieux, André et al. · Clin Infect Dis · 2005

case_report · Level V

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Abstract

Individuals with deficiencies of the late components of complement exhibit a susceptibility to the recurrence of meningococcal disease with a usually mild clinical presentation. We report the recurrence of fulminant meningococcal disease in a complement component C7-deficient patient. We found a total deficiency of FcgammaRIIIb on neutrophils, which could partially explain the unusually severe clinical presentation.

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