Survival in two variants of tau-negative frontotemporal lobar degeneration: FTLD-U vs FTLD-MND.

Josephs, K A; Knopman, D S; Whitwell, J L; Boeve, B F; Parisi, J E; Petersen, R C; Dickson, D W · Neurology · 2005

retrospective_cohort · Level III

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Abstract

Pathologic diagnoses in frontotemporal lobar degeneration (FTLD) include tau-positive FTLD and tau-negative FTLD. Two variants of tau-negative FTLD are FTLD with motor neuron disease (FTLD-MND) and FTLD with motor neuron disease type inclusions but without motor neuron disease (FTLD-U). An analysis of patient outcomes in these cases reveals that FTLD-MND has significantly shorter survival than FTLD-U, suggesting that FTLD-MND is a more aggressive disease process.

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