Klippel-Trenaunay syndrome with small vessel pulmonary arterial hypertension.

Ulrich, S; Fischler, M; Walder, B; Pfammatter, T; Speich, R · Thorax · 2005

case_report · Level V

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Abstract

A patient with Klippel-Trenaunay syndrome and pulmonary arterial hypertension not associated with chronic thrombo-embolic pulmonary hypertension is described. It is hypothesised that pulmonary arterial hypertension is another complication associated with the Klippel-Trenaunay syndrome, possibly due to haemodynamic changes of small vessel abnormalities.

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