Extramedullary hematopoiesis with spinal cord compression in beta-thalassemia intermedia.

Eur J Intern Med · 2005

case_report · Level V

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Abstract

Spinal cord compression due to extramedullary hematopoiesis is a rare manifestation of thalassemia. We present a 28-year-old woman with beta-thalassemia intermedia and progressive paraparesis. She had a thoracic extradural extramedullary mass lesion on MRI. She improved after receiving multiple transfusions. Clinical awareness of this phenomenon with early treatment is essential for a successful outcome.