Prenatal diagnosis of familial type I choledochal cyst.

Clifton, Matthew S; Goldstein, Ruth B; Slavotinek, Anne; Norton, Mary E; Lee, Hanmin; Farrell, Jody; Nobuhara, Kerilyn K · Pediatrics · 2006

case_report · Level V

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Abstract

Familial choledochal cysts are extremely rare. High-resolution ultrasound now allows for the antenatal diagnosis of these anomalies. After delivery, elective surgical resection should be planned; however, increases in size, deterioration of liver function, and ascending cholangitis frequently force early intervention. We report an unusual occurrence of siblings with type I choledochal cysts and review the existing literature on cause, genetics, classification, diagnosis, and management of this disease.

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