Lymphomatoid papulosis followed by large-cell lymphoma: immunophenotypical and genotypical analysis.

Kaudewitz, P; Herbst, H; Anagnostopoulos, I; Eckert, F; Braun-Falco, O; Stein, H · Br J Dermatol · 1991

case_report · Level V

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Abstract

The immunophenotype and genotype of atypical cells in skin and lymph node infiltrates were investigated in a patient with lymphomatoid papulosis (LyP) complicated by anaplastic large-cell lymphoma of the lymph nodes. The large atypical cells in both skin and lymph nodes displayed an almost identical immunophenotype, i.e. CD30+ and CD25+. Southern blot analysis for T-cell receptor beta-chain gene rearrangement revealed an identical gene configuration in DNA extracted from skin and lymph node. Our results strongly support the hypothesis that clonal populations of T cells arising in cutaneous LyP lesions may undergo malignant transformation, spread into regional lymph nodes, and give rise to secondary malignant lymphomas, such as anaplastic large-cell lymphoma.

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