Methionine metabolism and phenotypic variability in X-linked adrenoleukodystrophy.

Linnebank, M; Kemp, S; Wanders, R J A; Kleijer, W J; van der Sterre, M L T; Gärtner, J; Fliessbach, K; Semmler, A et al. · Neurology · 2006

case_control · Level III

Where this comes from

Abstract

A combined genotype of polymorphisms of methionine metabolism has been associated with CNS demyelination in methotrexate-treated patients. Within a sample of 86 patients with X-linked adrenoleukodystrophy, this genotype was overrepresented in a subgroup of 15 patients with adrenomyeloneuropathy (AMN) with CNS demyelination (adrenoleukomyeloneuropathy) in comparison to 49 AMN patients without CNS demyelination ("pure" AMN; p = 0.002), suggesting that methionine metabolism might contribute to the phenotypic variability in adrenoleukodystrophy.

Medical subject headings