Mucocutaneous bullous amyloidosis with an unusual mixed protein composition of amyloid deposits.
case_report · Level V
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- Record sourced from PubMed, PMID 16536823.
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Abstract
We describe a case of fatal systemic amyloidosis presenting with mucocutaneous bullous lesions in a patient with IgA kappa monoclonal gammopathy. The amyloid plaques were composed of an unusual mixture of immunoglobulin kappa light chain and amyloid A proteins. Whereas oesophageal and oropharyngeal blisters are known to occur in several types of bullous dermatoses, to our knowledge this is the first report of oesophagopharyngeal blisters complicating bullous amyloidosis.
Medical subject headings
- Amyloidosis
- Skin Diseases, Vesiculobullous