Mutations in the DNA mismatch repair gene MLH1 associated with early-onset colon cancer.

Marcos, Irene; Borrego, Salud; Urioste, Miguel; García-Vallés, Carmen; Antiñolo, Guillermo · J Pediatr · 2006

case_report · Level V

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Abstract

Hereditary nonpolyposis colon cancer (HNPCC) is an autosomal dominant disorder characterized by the predisposition to develop a number of cancers, especially colorectal cancer (CRC). We present a HNPCC family with CRC at age 12 years. Our observations suggest that the germline mutation of the both copies of the MLH1 gene may play a role in the early onset of CRC.

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