Cutaneous metastasis of pheochromocytoma in multiple endocrine neoplasia IIB.

Duquia, Rodrigo Pereira; de Almeida, Hiram Larangeira; Traesel, Moacir; Jannke, Heitor Alberto · J Am Acad Dermatol · 2006

case_report · Level V

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Abstract

Pheochromocytoma is a rare tumor originating from neuroectodermic cells. Only 10% of these tumors are malignant. There are many familial forms of this tumor, including multiple endocrine neoplasia type II, Von Hippel-Lindau syndrome, and neurofibromatosis type I. Skin manifestations of pheochromocytoma are rare, and cutaneous metastasis in patients with multiple endocrine neoplasia IIB has never been described. The case of a patient with multiple endocrine neoplasia IIB who presented malignant pheochromocytoma with multiple cutaneous metastasis is described.

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