Posterior correction and fusion for severe cervical kyphosis in a patient with myotonic dystrophy: a case report.

Abstract

A case report. To report the first myotonic dystrophy case in which cervical kyphosis had been surgically corrected. Myotonic dystrophy is an autosomal dominant disease that shows myotonia, progressive muscle atrophy, and other various symptoms. Instability of the neck is expected to cause disorders of the cervical spine; however, there are no detailed reports on deformity of cervical spine associated with this disease. A 43-year-old man with cervical kyphosis due to myotonic dystrophy had undergone an occiput-T2 fusion with autogenous iliac bone using spinal instrumentation. The activity of daily life of the patient had improved markedly, and the good results continued to be preserved for 5 years. There were not any major perioperative complications. Surgical correction of cervical spine is not necessarily a contraindication for myotonic dystrophy.