Charcot-Marie-Tooth disease due to a de novo mutation of the RAB7 gene.

Meggouh, F; Bienfait, H M E; Weterman, M A J; de Visser, M; Baas, F · Neurology · 2006

case_report · Level V

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Abstract

We report a 32-year-old patient with Charcot-Marie-Tooth (CMT2B) including foot ulcerations. Genetic analysis identified a de novo mutation in the small GTP-ase late endosomal RAB7 gene, consisting of a c.471G>C, p.Lys157Asn missense mutation. This observation strongly supports the hypothesis that RAB7 mutations are responsible for CMT2B.

Medical subject headings

Anatomy