The role of surgical biopsy in the diagnosis of glioma in individuals with neurofibromatosis-1.

Leonard, J R; Perry, A; Rubin, J B; King, A A; Chicoine, M R; Gutmann, D H · Neurology · 2006

case_series · Level IV

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Abstract

Most gliomas in neurofibromatosis type 1 (NF1) are pilocytic astrocytomas (PAs) of the optic pathway occurring in young children. However, some individuals develop gliomas that lack the typical NF1-associated clinical features or radiographic appearance. We identified 17 atypical presentations from a review of 100 patients with NF1-associated gliomas. Biopsy showed that 9 were not classic PAs. These data highlight the value of biopsy in NF1-associated gliomas with unusual clinical or radiographic presentations.

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