Genetic heterogeneity of autosomal dominant nonprogressive congenital ataxia.

Jen, J C; Lee, H; Cha, Y H; Nelson, S F; Baloh, R W · Neurology · 2006

case_series · Level IV

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Abstract

We studied a family with nonprogressive congenital ataxia (NPCA) previously reported in 1985. Follow-up evaluation documented a nonprogressive course. Older family members developed ataxic spells and vertical oscillopsia triggered by stress and exercise. Linkage analysis using a 10K single-nucleotide polymorphism array found suggestive linkage to four loci on chromosomes 1q44, 5q35.1-35.3, 7q36.2-36.3, and 9q31.2-32 and ruled out linkage to the NPCA locus on 3p, proving genetic heterogeneity for autosomal dominant NPCA.

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